FIBRODYSPLASIA OSSIFICANS PROGRESSIVA: A RARE ENTITY

Dr. Siddhant Bhardwaj, Dr. Nilesh Ingale, Dr. Madan Manmohan, Dr Kunal Arora, Dr Harsha Jeswani

Abstract


Myositis ossificans progressiva is a rare connective tissue disease characterized by widespread, progressive, heterotopic ossification of soft tissues, congenital skeletal anomalies and progressive ectopic bone formation. We report 2 cases which presented with complains of difficulty in walking, stiffness and pain in both hip joints since 15 years. CT reveals extensive bridging extra skeletal areas of sclerosis and ossification involving the soft tissue around the hip and lower extremities. Though rare, diagnosis of fibrodysplasia ossificans progressiva should be considered whenever characteristic radiographic features of multifocal heterotopic bone formation are seen. Early diagnosis is necessary to prevent its debilitating progression.

Keywords


Fibrodysplasia ossificans progressiva, Computed tomography, Heterotopic ossification

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